Dancing eye syndrome as first symptom of neuroblastoma

Dancing eye syndrome as first symptom of neuroblastoma

Authors

  • Cristina Venturelli Post-Graduate School of Pediatrics University of Modena and Reggio Emilia
  • Azzurra Guerra Pediatric Unit, Department of Medical and Surgical Sciences
  • Paolo Paolucci Post-Graduate School of Pediatrics Pediatric Unit University of Modena and Reggio Emilia
  • Lorenzo Iughetti Post-Graduate School of Pediatrics Pediatric Unit University of Modena and Reggio Emilia

Keywords:

Opsoclonus-Myoclonus Syndrome, dancing eye syndrome, neuroblastoma, paraneoplastic neurologic disorder

Abstract

Background: “Dancing eye syndrome”, also called Kinsbourne syndrome or Opsoclonus-Myoclonus-Ataxia Syndrome (OMS) is a rare neurological disorder that in children is frequently associated to occult, low-grade neuroblastoma (NB) (>50% of the cases). OMS may also be triggered by infections and it is often associated to developmental impairment and disability.

Case presentation: We discuss the case of a 16 months old female with acutely onset of OMS associated to occult stage III NB.

Conclusions: OMS represents a diagnostic challenge for pediatric clinicians. The suspect of OMS imposes the search for an occult NB in order to promptly treat a life-threatening event like tumor and to prevent the neurological sequels linked to OMS.

Downloads

Published

01-09-2013

Issue

Vol. 84 No. 2 (2013)

Section

CASE REPORTS

License

This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Transfer of Copyright and Permission to Reproduce Parts of Published Papers. 
Authors retain the copyright for their published work. No formal permission will be required to reproduce parts (tables or illustrations) of published papers, provided the source is quoted appropriately and reproduction has no commercial intent. Reproductions with commercial intent will require written permission and payment of royalties.

How to Cite

1.
Venturelli C, Guerra A, Paolucci P, Iughetti L. Dancing eye syndrome as first symptom of neuroblastoma. Acta Biomed [Internet]. 2013 Sep. 1 [cited 2024 Jul. 27];84(2):162-6. Available from: https://mattioli1885journals.com/index.php/actabiomedica/article/view/2726