A case of relapsing isolated neurosarcoidosis in an 18-year-old male patient successfully treated by corticosteroids

A case of relapsing isolated neurosarcoidosis in an 18-year-old male patient successfully treated by corticosteroids

Authors

  • Klaudia Kalmárová Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Egon Kurča Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Štefan Sivák Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Jozef Michalik Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Lukáš Plank Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin
  • Róbert Vyšehradský Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Kamil Zeleňák Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Juraj Šutovský Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava
  • Vladimir Nosáľ Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Keywords:

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Abstract

Sarcoidosis is a granulomatous multisystemic disease of unknown cause most often affecting the lungs, lymph nodes of the pulmonary hilus, eyes, skin, and other structures including central (CNS) or peripheral nervous system (PNS). Isolated neurosarcoidosis is extremely rare. The diagnosis of isolated neurosarcoidosis is challenging because of its rarity, variety of manifestations, and the lack of systemic signs.  We report relapsing and remitting isolated intracranial neurosarcoidosis in an 18-year-old male patient who undervent complex diagnostics including cerebral and meninges biopsy. Patient was succesfully treated with corticosteroids.

Author Biographies

Klaudia Kalmárová, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurology

Egon Kurča, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurology

Štefan Sivák, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurology

Jozef Michalik, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurology

Lukáš Plank, Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin

Department of Pathological Anatomy

Róbert Vyšehradský, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Pneumology and Phthisiology

Kamil Zeleňák, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Radiology

Juraj Šutovský, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurosurgery

Vladimir Nosáľ, Jessenius Faculty of Medicine in Martin, Commenius University in Bratislava

Clinic of Neurology

 

 

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Published

11-03-2019

Issue

Section

Case Reports

How to Cite

1.
Kalmárová K, Kurča E, Sivák Štefan, Michalik J, Plank L, Vyšehradský R, et al. A case of relapsing isolated neurosarcoidosis in an 18-year-old male patient successfully treated by corticosteroids. Sarcoidosis Vasc Diffuse Lung Dis [Internet]. 2019 Mar. 11 [cited 2025 Mar. 9];36(1):79-85. Available from: https://mattioli1885journals.com/index.php/sarcoidosis/article/view/7168