Solely lung-involved IgG4-related disease : a case report and review of the literature

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Xiao-Qin Zhang
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Guo-Ping Chen
Department of Endocrinology, The First Affiliated Hospital, College of Medicine, Zhejiang University, Hangzhou 310003, China

Sheng-Chang Wu
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Sa Yu
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Hong Wang
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Xuan-Yi Chen
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Zhuo-Chao Ren
Department of Respirology, Zhejiang Provincial People’s Hospital, Hangzhou 310014, China

Keywords

IgG4-related disease, Immunoglobulin G4, Lung

Abstract

By analyzing the clinical data of 1 case of IgG4-related lung disease(IgG4-RLD) and the review of literature, the author investigated the clinical characteristics of IgG4-RLD. IgG4-RLD is a rare disease characterized by significant elevation of serum IgG4 and infiltration of a large number of IgG4+ plasma cells. The clinical manifestations of the disease were nonspecific, and the imaging features were mixed with several types. The disease can only be involved in the lung, but also multiple organ involvement. Solely lung-involved IgG4-RD is not only extremely rare but also easily misdiagnosed as tuberculosis, lung cancer, lymphoma and other common pulmonary diseases. Histopathological examination is the key to the diagnosis of the disease. Corticosteroids are the first choice of treatment, and the overall prognosis is good.
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Published
Dec 23, 2016

Article Details

How to Cite

1.
Zhang X-Q, Chen G-P, Wu S-C, Yu S, Wang H, Chen X-Y, et al. Solely lung-involved IgG4-related disease : a case report and review of the literature. Sarcoidosis Vasc Diffuse Lung Dis [Internet]. 2016 Dec. 23 [cited 2024 Dec. 20];33(4):398-406. Available from: https://mattioli1885journals.com/index.php/sarcoidosis/article/view/4785
Issue
Vol. 33 No. 4 (2016)
Section
Case Reports

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How to Cite

1.
Zhang X-Q, Chen G-P, Wu S-C, Yu S, Wang H, Chen X-Y, et al. Solely lung-involved IgG4-related disease : a case report and review of the literature. Sarcoidosis Vasc Diffuse Lung Dis [Internet]. 2016 Dec. 23 [cited 2024 Dec. 20];33(4):398-406. Available from: https://mattioli1885journals.com/index.php/sarcoidosis/article/view/4785