Bonebridge implantation for mixed hearing loss in a patient with Kabuki syndrome

Giovanni Pepe; Maurizio Negri; Maurizio Falcioni; Filippo Di Lella; Vincenzo Vincenti

doi:10.23750/abm.v91i3.8257

Bonebridge implantation for mixed hearing loss in a patient with Kabuki syndrome

Authors

Giovanni Pepe Otolaryngology and Otoneurosurgery Department, Azienda Ospedaliero-Universitaria di Parma, Via Gramsci 14, 43126 Parma, Italy.
Maurizio Negri Department of Otorhinolaryngology, Ospedale Ramazzini, Carpi, Italy
Maurizio Falcioni Otolaryngology and Otoneurosurgery Department, Azienda Ospedaliero-Universitaria di Parma, Via Gramsci 14, 43126 Parma, Italy.
Filippo Di Lella Otolaryngology and Otoneurosurgery Department, Azienda Ospedaliero-Universitaria di Parma, Via Gramsci 14, 43126 Parma, Italy
Vincenzo Vincenti Otolaryngology and Otoneurosurgery Department, Azienda Ospedaliero-Universitaria di Parma, Via Gramsci 14, 43126 Parma, Italy

DOI: https://doi.org/10.23750/abm.v91i3.8257

Keywords:

Kabuki syndrome; chronic otitis media; hearing loss; active middle ear implant

Abstract

The high prevalence of middle ear disease with related hearing loss in Kabuki syndrome requires the diagnostic and treatment expertise of otologists. This case report describes outcomes and changes in the quality of life of a patient affected by Kabuki syndrome with a history of recalcitrant chronic otitis media and mixed hearing loss who had undergone several unsuccessful surgical procedures before solving his problems by means of subtotal petrosectomy and active middle ear implant.

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Published

07-09-2020

Issue

Vol. 91 No. 3 (2020): COVID-19 Update

Section

CASE REPORTS

License

This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

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How to Cite

Pepe G, Negri M, Falcioni M, Di Lella F, Vincenti V. Bonebridge implantation for mixed hearing loss in a patient with Kabuki syndrome. Acta Biomed. 2020;91(3):e2020079. doi:10.23750/abm.v91i3.8257

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