Bonebridge implantation for mixed hearing loss in a patient with Kabuki syndrome

Main Article Content

Giovanni Pepe
Maurizio Negri
Maurizio Falcioni
Filippo Di Lella
Vincenzo Vincenti


Kabuki syndrome; chronic otitis media; hearing loss; active middle ear implant


The high prevalence of middle ear disease with related hearing loss in Kabuki syndrome requires the diagnostic and treatment expertise of otologists. This case report describes outcomes and changes in the quality of life of a patient affected by Kabuki syndrome with a history of recalcitrant chronic otitis media and mixed hearing loss who had undergone several unsuccessful surgical procedures before solving his problems by means of subtotal petrosectomy and active middle ear implant. 


Download data is not yet available.
Abstract 194 | PDF Downloads 106

Most read articles by the same author(s)