An unusual cause of Steven-Johnson Syndrome

An unusual cause of Steven-Johnson Syndrome

Authors

  • Claudia De Guido Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Adriana Calderaro Department of Medicine and Surgery, University of Parma, Parma, Italy
  • Maria Beatrice Ruozi Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Valentina Maffini Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Margherita Varini Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Irene Lapetina Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Monica Rubini Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Sara Montecchini Department of Medicine and Surgery, University of Parma, Parma, Italy
  • Carlo Caffarelli Clinica Pediatrica, Department of Medicine and Surgery, University of Parma, Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
  • Icilio Dodi Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy

Keywords:

Steven-Johnson Syndrome, allergy, enterovirus, corticosteroids, cyslosporine A

Abstract

SJS is a rare mucocutaneous syndrome characterized by skin and mucous detachment. The main etiological factors are drugs and infections; sometimes the cause remains unknown. In the prodromal phase we observed non-specific symptoms, followed by mucocutaneous manifestation. Due to risk of complications and mortality a multidisciplinary approach is needed.  We present a case of a girl with an atypical presentation of SJS related to Enterovirus.

Downloads

Published

19-03-2020

Issue

Section

CASE REPORTS

How to Cite

1.
An unusual cause of Steven-Johnson Syndrome. Acta Biomed [Internet]. 2020 Mar. 19 [cited 2024 Mar. 29];91(1):128-31. Available from: https://mattioli1885journals.com/index.php/actabiomedica/article/view/7692