Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient

Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient

Authors

  • Maria Teresa Paparella
  • Laura Eusebi
  • Roberta Mazzucchelli
  • Giuseppe Guglielmi

Keywords:

malignant peripheral nerve sheath tumors (MPNSTs), soft tissue sarcomas (STS), neurofibromatosis type I (NF-1), prognosis

Abstract

Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue sarcoma that originate from peripheral nerves or from cells associated with the nerve sheath. We report the case of a 30‑year‑old male patient with a history of neurofibromatosis type I (NF-1) and a MPNST located in the lumbar region. The mass was resecated but surgical margins weren’t clear. Recurrence of disease was observed after few months. A close monitoring of subjects with NF-1 is crucial to diagnose MPNST at an earlier stage and allow a complete surgical resection.

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Published

14-04-2022

Issue

Section

Case Reports: Oncology and Hematology

How to Cite

1.
Paparella MT, Eusebi L, Mazzucchelli R, Guglielmi G. Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient. Acta Biomed [Internet]. 2022 Apr. 14 [cited 2024 Jul. 13];93(S1):e2022095. Available from: https://mattioli1885journals.com/index.php/actabiomedica/article/view/12360